Hyperbilirubinemia
- Increased Unconjugated Bilirubin
- Jaundice
- Kernicterus
- Early Feedings
- Heme Oxygenase Inhibitors
- Phototherapy
- Protect Eyes
- Monitor for Dehydration
- Monitor Bilirubin Levels
Beta Thalassemia
- Microcytic, Hypochromic Anemia
- Mediterranean Populations
- Decreased Beta-Globin
- Increased HbA2
- No Intervention
- Blood Transfusions
- Hemochromatosis
- Crew-cut on Skull X-Ray
- Electrophoresis
Sickle Cell Anemia (Mechanism)
- Intrinsic Normocytic Hemolytic Anemia
- Point Mutation
- Autosomal Recessive
- African-American
- Dehydration or Decreased O2
- Newborns Asymptomatic
- Heterozygote Malarial Resistance
Sickle Cell Anemia (Signs and Complications)
- Crew-cut on Skull X-ray
- Auto-splenectomy
- Painful Crisis
- Aplastic Crisis
- Splenic-sequestration Crisis
- Hyper-hemolytic Syndrome
- Renal Papillary Necrosis
- Salmonella osteomyelitis
- Pulmonary Hypertension
- Hyposthenuria
Sickle Cell Anemia (Management)
- Hydroxyurea
- Bone Marrow Transplant
- Folate
- Exchange Transfusion
- Penicillin Prophylaxis
Hemolytic Uremic Syndrome (HUS)
- Children
- Preceded by Acute Diarrheal Illness
- Endothelial Damage
- Microangiopathic Hemolytic Anemia (MAHA)
- Thrombocytopenia
- Renal Failure
- Helmet cells
- LDH
- Dialysis
- Supportive
Hereditary Spherocytosis Disease
- Northern Europeans
- Autosomal Dominant
- Spectrin/Ankyrin Deficiency
- Spherocyte Formation
- Hemolytic Anemia
- Bilirubin Gallstones
- Jaundice
- Splenomegaly
Hereditary Spherocytosis Diagnosis & Treatment
- Increased MCHC
- Spherocytes
- Normocytic Anemia
- Eosin-5-Maleimide (EMA) Binding Test
- Osmotic Fragility Test
- Glycerol Lysis Test
- Folic Acid
- Splenectomy
Fanconi Anemia
- Autosomal Recessive
- Aplastic Anemia
- DNA Crosslink Repair Defect
- Short Stature
- Microcephaly
- Thumb and Forearm Malformations
- Cafe Au Lait Spots
- Ocular Abnormalities
- Horseshoe Kidney
- Chromosomal Breakage Testing
- Macrocytic Anemia
- Pancytopenia
- Monitor For Malignancy and Bone Marrow Failure
- Hematopoietic Stem Cell Transplantation