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Maternity and Women's Health Care, 12th Ed., Lowerdermilk, Perry, Cashion & Aldon, 2020
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36 - Hemolytic Disorders and Congenital Anomalies

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Maternity and Women's Health Care, 12th Ed., Lowerdermilk, Perry, Cashion & Aldon, 2020 | Registered Nurse (RN) School Study Aid

36 - Hemolytic Disorders and Congenital Anomalies
12 Picmonics to Learn | 22 mins
Aortic Regurgitation
Auscultation
Diastolic Murmur
Immediate High-pitched
Blowing Murmur
Clinical Findings
Wide Pulse Pressure
Water Hammer Pulse
Head Bobbing
Pulsating Nail Bed
Considerations
Can Cause Austin Flint Murmur
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1 min
Tetralogy of Fallot (TOF)
Features
Blue Baby Syndrome
Mechanism
PROVe Acronym
Pulmonary Infundibular Stenosis
Right Ventricular Hypertrophy
Overriding Aorta
Ventricular Septal Defect (VSD)
Diagnosis and Treatment
Boot-Shaped Heart
Squatting for Tet Spells
Surgery
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2 mins
RhoGam [Rho(D) Immune Globulin]
Indications
Antepartum Prevention at 28 weeks
Suppress Antibody Production
Mechanism of Action
Lysis of Fetal RBC in Maternal Bloodstream
Side Effects
Myalgia and Lethargy
Considerations
Negative Coombs Test
Standard Dose 300 mcg
Microdose 50 mcg
Blood Product
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2 mins
Aortic Stenosis
Characteristics
Age-related Calcifications
Bicuspid Aortic Valve
Crescendo-decrescendo Murmur
Systolic Murmur
Ejection Murmur
Ejection Click
Radiates to Carotids and Apex
Pulsus Parvus et Tardus
Syncope
Helmet Cells
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2 mins
Patent Ductus Arteriosus
Continuous
Machine like murmur
Often Due to Congenital Rubella
Prematurity
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1 min
Blood Types and Compatibilities
ABO Compatibility
No Antigens (Type O Blood)
Universal Donor
A Antigen (Type A Blood)
B Antigen (Type B Blood)
AB Antigen (Type AB Blood)
Universal Recipient
Rhesus (Rh) Compatibility
Rh (Rhesus) Antigen
Never Rh+ to Rh-
Considerations
Blood Transfusion
Obstetric Patient
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2 mins
Spina Bifida Assessment
Cause
Congenital Malformation of Vertebrae
Assessment
Dimple With or Without Hair Tuft
Lumbar Sac
Hydrocephalus
Paralysis
Considerations
Identify Type
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2 mins
Spina Bifida Interventions
Surgery
Prone Position
Cover Sac with Moist (Sterile) Dressing
Measure Head Circumference
Bulging Fontanel
Considerations
Other Congenital Malformations Common
Bowel Control
Neurogenic Bladder
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2 mins
Hydrocephalus
Cause
Increased CSF in Ventricles of Brain
Assessment
Signs of Increased ICP
Infant Assessment
High Pitched Cry
Irritability
Opisthotonus
Increased Head Circumference
Bulging Fontanel
Setting Sun Sign
Interventions
Seizure Precautions
Elevate HOB
CSF Shunt
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2 mins
Cleft Lip or Palate Interventions
Considerations
Encourage Bonding
Prosthodontic Device
Modified Nipple
Burping
Surgical Repair
Normal Saline Rinse
Elbow Restraints
Avoid Rigid Eating Utensils
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2 mins
Tracheoesophageal Fistula (TEF)
Cause
Esophageal Atresia
Ends in Blind Pouch
Assessment
Coughing
Choking
Cyanosis
Drooling
Considerations
NPO
Surgical Emergency
Aspiration Pneumonia
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2 mins
Imperforate Anus
Mechanism
Congenital Anorectal Malformation
Signs and Symptoms
No Anal Opening
Absence of Meconium
Gradual Increase in Abdominal Distention
Considerations
Surgical Repair
Bowel Management
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2 mins

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