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Jack Shared "Heme/Onc Block" - 10 Picmonics

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Heme/Onc Block

Tumor Lysis Syndrome
Characteristics
Leukemia/Lymphoma Treatment
Oncologic Emergency
Clinical Features
GI Distress
Fatigue
Arrhythmias
Acute Kidney Injury
Lab Findings
Hyperkalemia
Hyperphosphatemia
Hyperuricemia
Hypocalcemia
Management
Aggressive Hydration
Electrolyte Correction
Allopurinol
Rasburicase
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3 mins
Anemia Lab Values
Iron Deficiency Anemia
Serum Iron Decreased
Transferrin Increased
Ferritin Decreased
% Transferrin Saturation Decreased
Pregnancy and OCP Use
Serum Iron Normal
Transferrin Increased
Ferritin Normal
% Transferrin Saturation Decreased
Anemia of Chronic Disease
Serum Iron Decreased
Transferrin Decreased
Ferritin Increased
% Transferrin Saturation Decreased or Normal
Hemochromatosis
Serum Iron Increased
Transferrin Decreased
Ferritin Increased
% Transferrin Saturation Increased
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3 mins
Fanconi Anemia
Characteristics
Autosomal Recessive
Aplastic Anemia
DNA Crosslink Repair Defect
Clinical Presentation
Short Stature
Microcephaly
Thumb and Forearm Malformations
Cafe Au Lait Spots
Ocular Abnormalities
Horseshoe Kidney
Lab Findings
Chromosomal Breakage Testing
Macrocytic Anemia
Pancytopenia
Management
Monitor For Malignancy and Bone Marrow Failure
Hematopoietic Stem Cell Transplantation
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3 mins
ABO Hemolytic Disease of the Fetus and Newborn
Characteristics
ABO Incompatibilities
Type O Mother and Type A/B Fetus
Anti-A or Anti-B Antibodies
Hemolytic Anemia
Presentation
Often Asymptomatic
Neonatal Jaundice
Diagnosis
Negative Coombs Test
Management
Phototherapy
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2 mins
Rh Hemolytic Disease of the Fetus and Newborn
Characteristics
Rh (Rhesus) Incompatibilities
Rh(D)- Mother and Rh(D)+ Fetus
Anti-Rh(D) Antibodies
Hemolytic Anemia
Presentation
Hydrops Fetalis
Neonatal Jaundice
Kernicterus
Diagnosis
Positive Coombs Test
Ultrasound
Management
RhoGAM [Anti-Rh(D) Immunoglobulin]
Intrauterine Blood Transfusion
Phototherapy
IVIG (Intravenous Immunoglobulin)
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4 mins
Diamond-Blackfan Anemia
Characteristics
Red Blood Cell Aplasia
Macrocytic Anemia
Clinical Features
Short Stature
Craniofacial Anomalies
Triphalangeal Thumbs
Diagnosis
Increased HbF (Fetal Hemoglobin)
Management
RBC Transfusion
Steroids
Hematopoietic Stem Cell Transplantation
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2 mins
Mycosis Fungoides / Sézary Syndrome
Mechanism
Neoplastic CD4+ Cells
Adults 40 - 60 Years Old
Mycosis Fungoides
Neoplastic CD4+ Cells Infiltrate Skin
Rashes Or Plaques
Pautrier's Abscesses
Sézary Syndrome
Neoplastic CD4+ Spread from Skin to Systemic Involvement
Sézary Cells With "Cerebriform Nuclei"
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2 mins
Langerhans Cell Histiocytosis
Characteristics
Antigen Presentation Defect
Lytic Bone Lesions
Skull
Presentation
Hypopituitarism
Diabetes Insipidus
Skin Rash
Recurrent Otitis Media
Diagnosis
Birbeck Granules
"Tennis Racket" Appearance
S100 Positive
Management
Observation
Prednisone +/- Vinblastine
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4 mins
Hemophagocytic Lymphohistiocytosis
Characteristics
Excessive Immune System Activation
Cytotoxic T-cells and Macrophages
Cytokine Storm
Acquired or Sporadic
Presentation
Fever
Hepatosplenomegaly
Labs
Increased Ferritin
Pancytopenia
Management
Bone Marrow Transplantation
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3 mins
Fanconi Anemia
DNA repair defect in nonhomologous end joining
Aplastic Anemia
Short stature
increased incidence of tumors/leukemia
café-au-lait spots
defective or absent thumbs
Autosomal recessive
More Common in Ashkenazi Jewish Population
Microcephaly
Microphthalmia
Horseshoe Kidney
Pancytopenia
macrocytosis
X-linked
Hypogonadism
large freckles
strabismus (cross-eyed)
Low-Set Ears
Deafness
pou
pounding in ears (d/t hemorrhage or conduction defects or middle ear abnormalities)
hematopoietic stem cell transplant to treat
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Jack Shared Heme/Onc Block - 10 Picmonics