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Wayne Shared "Pathology Bliss 6/20/2024" - 50 Picmonics

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Pathology Bliss 6/20/2024

Acute Lymphoblastic Leukemia (ALL)
Ages < 15
May Present with Bone Marrow Involvement in Children
Mediastinal Mass in Adolescents
TdT Positive
CALLA Positive
t(12;21) Better Prognosis
Spread to CNS and Testes
Most Responsive to Chemotherapy
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2 mins
Acute Myelogenous Leukemia (AML)
Myeloblasts Increase on Peripheral Smear
Median Onset 60 Years
T 15;17 M3 Subtype
Auer Rods
Disseminated Intravascular Coagulation (DIC) is a Common Presentation
M5 Gum Infiltration
Responds to Vitamin A
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3 mins
Polycythemia Vera Disease
Pathophysiology
JAK2 Mutation leading to increased red blood cells
Tyrosine Kinase
Symptoms
Erythromelalgia
Pruritus
Often After Hot Shower
Headache
Treatment
Phlebotomy
Aspirin
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1 min
Polycythemia Vera Labs
Lab Findings (The 4 H's)
Hypervolemia
Histaminemia
Hyperviscosity
Hyperuricemia
Diagnosis
Elevated Hemoglobin or Hematocrit
Positive Jak2 Mutation
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1 min
Blood Cancer Overview
Acute Conditions
Acute Lymphoblastic Leukemia (ALL)
Acute Myeloid Leukemia (AML)
Chronic Conditions
Chronic Lymphocytic Leukemia (CLL)
Adult T Cell Lymphoma
Chronic Myeloid Leukemia (CML)
Blast Crisis
Polycythemia Vera Disease
Essential Thrombocythemia
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4 mins
Chronic Myelogenous Leukemia (CML)
Pathophysiology
BCR-ABL
9;22 Translocation
Philadelphia Chromosome
Signs & Symptoms
Tyrosine Kinase
Low Alkaline Phosphatase
Splenomegaly
Considerations
Blast Crisis
Age 30 to 90 Years
Responds to Imatinib
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3 mins
Essential Thrombocythemia
Characteristics
JAK2 Mutation
Presentation
Often Asymptomatic
Thromboembolic Events
Spontaneous Abortion
Erythromelalgia
Gout
Diagnosis
Thrombocytosis
Megakaryocyte Hyperplasia
Management
Aspirin
Hydroxyurea
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2 mins
Imatinib (Gleevec)
Indications
Chronic Myelogenous Leukemia (CML)
Inhibitor of BCR-ABL Tyrosine Kinase
Caused by Philadelphia Chromosome
GI Stromal Tumors
Inhibitor of C-kit Tyrosine Kinase
Toxicity
Fluid Retention
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1 min
Primary Myelofibrosis
Characteristics
Bone Marrow Fibrosis
Extramedullary Hematopoiesis
JAK2 Kinase Mutation
Symptoms
Fatigue
Weight Loss
Splenomegaly
DIagnosis
Pancytopenia
Dacrocytes (Teardrop Cells)
Dry Tap on Bone Marrow Aspiration
Treatment
Stem Cell Transplantation
Transfusion
Ruxolitinib (JAK2 Inhibitor)
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2 mins
Lichen Simplex Chronicus
Pathophysiology
Hyperplasia of Vulvar Squamous Epithelium
Scratching
Rubbing
Benign
No Risk of Squamous Cell Carcinoma
Signs and Symptoms
Leather Skin
Pruritus
Management
Corticosteroids
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1 min
Extramammary Paget disease of the VULVA- (with Audio)
Microscopic features
Malignant epithelial cells in the epidermis of the vulva
pale/clear cytoplasm in pagetoid cells
"Large pleomorphic cells"
eccentric nuclei
Pagetoid spread histology picture
General
not Melanoma....
erythematous, pruritic, ulcerated vulvar lesion
No underlying carcinoma,
Markers
PAS + stain
Keratin Positive
S100 negative
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8 mins
Squamous Cell Carcinoma of the Skin
Epidemiology
2nd Most Common Skin Cancer
UV Light Exposure
Long-term Immunosuppression
Arsenic Exposure
Signs/Symptoms
Ulcerative Red Lesion
Precursor Actinic Keratosis
Commonly Lower Lip
Diagnosis
Biopsy shows Keratin Pearls
Treatment
Mohs Micrographic Surgery
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2 mins
Vaginal Cancer Subtypes
Squamous Cell Carcinoma
Squamous Cell Carcinoma
Most Common Subtype
Associated with Cervical Squamous Cell Carcinoma
Clear Cell Adenocarcinoma
Clear Cell Adenocarcinoma
Diethylstilbestrol (DES) Exposure
Sarcoma Botryoides
Sarcoma Botryoides
Malignant Rhabdomyosarcoma
"Bunch of Grapes" in Vagina
Spindle-Shaped Cells
Desmin Positive
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3 mins
Vaginal Cancer
Characteristics
HPV 16, 18
Squamous Cell Carcinoma is Most Common Subtype
Clinical Features
Vaginal Bleeding
Leukoplakia
Diagnosis
Colposcopy with Biopsy
Management
Radiation Therapy
Surgery
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2 mins
Embryonal Rhabdomyosarcoma (Sarcoma Botryoides)
Immature skeletal muscle
Bleeding grape like mass
Desmin and myogenin
Cytoplasm resemble tennis racket
Invade into peritoneum and urinary tract
Surgery and chemotherapy
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Pelvic Inflammatory Disease (PID)
Mechanism
Neisseria gonorrhoeae
Chlamydia Trachomatis
Symptoms
Cervical Motion Tenderness
Chandelier Sign
Salpingitis
Tubo-ovarian abscess
Hydrosalpinx
Complications
Ectopic Pregnancy
Infertility
Adhesions
Fitz-Hugh-Curtis Syndrome
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2 mins
Neisseria gonorrhoeae Disease
Signs & Symptoms
Dysuria
Pelvic Inflammatory Disease (PID)
Fitz-Hugh-Curtis Syndrome
Neonatal Conjunctivitis
Pharyngitis
Septic Arthritis
Tenosynovitis
Pustules On Hands And Feet
Treatment
Ceftriaxone
Azithromycin
Doxycycline
Considerations
C5-9 Complement Deficiency (Recurrent Infections)
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2 mins
Paclitaxel (Taxanes)
Mechanism of Action
Taxane
Stabilizes Microtubules
Indications
Breast Cancer
Ovarian Cancer
Non-Small Cell Lung Cancer
Kaposi Sarcoma (HHV-8)
Side Effects
Mucositis
Myelosuppression
Peripheral Neuropathy
Hypersensitivity
Alopecia
Considerations
Diphenhydramine (Benadryl)
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2 mins
Polycystic Ovarian Syndrome (PCOS) Mechanism
Mechanism
Hyperinsulinemia Increases GnRH Pulse Frequency
Large Increase in LH
Small Decrease in FSH
Increased Androgen Production From Theca-Lutein Cells
Decreased Steroid Hormone-Binding-Globulin (SHBG) Causes Increased Free Testosterone
Obese Patients Have Increased Estrogen
Increased Risk of Endometrial Cancer
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2 mins
Polycystic Ovarian Syndrome (PCOS) Symptoms and Diagnosis
Symptoms
Most Common Cause of Infertility in Women
Amenorrhea
Acne
Hirsutism
Obesity
Diagnosis
Enlarged, Cystic Ovaries
LH:FSH Ratio of 3:1
"String of Pearls" on Ultrasound
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1 min

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