Zollinger-Ellison Syndrome Disease
Gastrin-Secreting Tumor Increased Gastric Acid Recurrent Peptic Ulcers MEN Type 1 Abdominal Pain Heartburn (Pyrosis) Diarrhea Celiac Disease Diagnosis and Treatment
Blunting of Intestinal Villi Lymphocytes in Lamina Propria Anti-gliadin Antibodies (IgA) Anti-endomysial Antibodies (IgA) Anti-tissue Transglutaminase Antibodies (IgA) Gluten-Free Diet Corticosteroids Dapsone Intestinal Lymphoma Stomach Cancer
Adenocarcinoma Intestinal Type Smoked Foods Containing Nitrosamines Achlorhydria Type A Blood Helicobacter pylori Diffuse Type Signet Ring Cells Linitis Plastica (Leather Bottle Stomach) Acanthosis Nigricans Left Supraclavicular Lymph Node Virchow's Node Subcutaneous Periumbilical Mets Sister Mary Joseph's Nodule Bilateral mets to ovaries Krukenberg's tumor Whipple's Disease
Tropheryma Whipplei Gram-Positive Middle-aged, Caucasian men and Farmers Malabsorption Mesenteric Nodes Arthralgias Cardiac Symptoms Neurologic Symptoms PAS-positive Foamy Macrophages Crohn's Disease Characteristics
Terminal Ileum and Colon Rectal Sparing Transmural Inflammation Granulomas Skip Lesions Cobblestone Mucosa Fissures Fistulas Perianal Disease Creeping Fat Lymphoid Aggregates String Sign on Barium Swallow Crohn's Symptoms and Associations
Diarrhea Malabsorption Bile-Wasting Pigment Gallstones Oxalate Kidney Stones Ankylosing Spondylitis Erythema Nodosum Uveitis Migratory Polyarthritis Ulcerative Colitis Characteristics
Autoimmune Mucosal and Submucosal Only Rectal Involvement Stepwise Lesions Friable Pseudopolyp Crypt Abscess Loss of Haustra Lead Pipe Appearance Bloody Diarrhea Ulcerative Colitis Associations
Toxic Megacolon Colorectal Carcinoma Anterior Uveitis Pyoderma Gangrenosum Ankylosing Spondylitis Primary Sclerosing Cholangitis P-ANCA Carcinoid Syndrome
Neuroendocrine Cells Serotonin Appendix Chromogranin A Neuron Specific Enolase Dense Core Bodies on EM Symptoms When Metastasize to Liver Flushing Wheezing Right Heart Murmur Diarrhea Peutz-Jeghers Syndrome
Symptomatic Age: 10-30 Years LKB1/STK11 Gene Mutation Autosomal Dominant Benign GI Hamartomatous Polyps Mucocutaneous Hyperpigmentation Positive Family History Increased Risk of Colorectal Carcinoma Lynch Syndrome (Hereditary Nonpolyposis Colorectal Cancer)
Autosomal Dominant Defective DNA Mismatch Repair 80% Risk of Colon Cancer Development Proximal (Right) Colon Type II associated with Endometrial, Ovarian and Skin Cancers 3 Relatives with Colon Cancer Occurs Across 2 Generations 1 Relative Diagnosed < 50 Years Old Frequent Screening Colectomy Ranson's Criteria on Admission
Mortality Predictor for Acute Pancreatitis GA LAW (Each is +1) Glucose > 200 mg/dL Age > 55 Years LDH > 350 U/L AST > 250 U/L WBC Count > 16,000/mm3 Ransons Criteria During First 48 Hours
Mortality Predictor for Acute Pancreatitis C HOBBS (Each is +1) Calcium < 8.0 mg/dL Hematocrit Decreased by > 10% Oxygen (PO2) < 60 mmHg BUN Increased by Greater or Equal to 5 mg/dL Base Deficit > 4 mEq/L Sequestered Fluid > 6 L Primary Biliary Cholangitis (Primary Biliary Cirrhosis) Diagnosis and Treatment
Positive Antimitochondrial Antibodies Increased Alkaline Phosphatase (ALK-P) Increased Cholesterol Ursodiol Liver Transplant Primary Biliary Cholangitis (Primary Biliary Cirrhosis)
Autoimmune Destruction of Bile Ducts Intrahepatic bile ducts Cholestasis Occurs in Middle-Aged Females Fatigue Pruritus Skin Hyperpigmentation Hepatomegaly Primary Sclerosing Cholangitis Labs and Treatment
Increased Conjugated Bilirubin Increased ALK-P Increased IgM Ulcerative Colitis Cholangiocarcinoma Secondary Biliary Cirrhosis Liver Transplant Stent Primary Sclerosing Cholangitis Mechanisms
Unknown Mechanism "Onion Skin" Fibrosis "Beading" of Bile Ducts Pruritus Hepatosplenomegaly Jaundice Crigler-Najjar Syndrome Type 1
Autosomal Recessive Absent UDP-glucuronosyltransferase Neonatal Jaundice Kernicterus Normal Liver Function Tests Elevated Unconjugated Bilirubin Phototherapy Plasmapheresis Calcium Phosphate and Orlistat Death often by Age 2 No Response to Phenobarbital Gilbert's Syndrome
Decreased UDP-Glucuronosyltransferase Activity Decreased Bilirubin Conjugation Often Asymptomatic Jaundice (Mild) Fasting Stress Alcohol Intake Increased Unconjugated Bilirubin Hemochromatosis Signs and Symptoms
Micronodular Cirrhosis Hepatocellular Carcinoma Diabetes Bronze Skin Coloring CHF Arthropathy Testicular Atrophy Impotence View More
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