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Spina Bifida Assessment
Cause
Congenital Malformation of Vertebrae
Assessment
Dimple With or Without Hair Tuft
Lumbar Sac
Hydrocephalus
Paralysis
Considerations
Identify Type
2 mins
Clubfoot
Cause/Mechanism
Multifactorial Congenital Anomalies
Fetal Position
Assessment
Deformed Foot and Ankle Position
Talipes Equinovarus
Interventions
Serial Casting
Ponseti Method
Early Surgery
2 mins
Left-to-Right Heart Shunts
The 3 Ds
Ventricular Septal Defect (VSD)
Atrial Septal Defect (ASD)
PDA
Associations
Later Cyanosis
Clubbing
Eisenmenger's Syndrome
2 mins
Right to Left Heart Shunts
The 5 Ts
Truncus Arteriosus
Transposition of the Great Vessels
Tricuspid Atresia
Tetralogy of Fallot
Total Anomalous Pulmonary Venous Return (TAPVR)
Associations
Cyanosis at Birth
May Require PDA
1 min
Cerebral Palsy (CP)
Cause/Mechanism
Maternal Infections
Fetal Hypoxia
Assessment
Developmental Delay
Neurological Dysfunction
Spasticity
Dysphagia
Interventions
Muscle Relaxants
Muscle Exercises
Assistive Devices
Braces
2 mins
Respiratory Syncytial Virus (RSV) Interventions
Prophylaxis
Palivizumab (Synagis)
Management
Hospitalization
Contact Precautions
Oxygen
Separate Room
Maintain Fluid Intake
Short-acting Beta-Agonist Bronchodilator
2 mins
Croup (Laryngotracheobronchitis)
Mechanism
Parainfluenza Virus
Assessment
3 Months to 3 Years
Nighttime
Barking Seal Cough
Inspiratory Stridor
Interventions
Cool Humidified Air
Dexamethasone
Racemic Epinephrine
2 mins
Cystic Fibrosis Assessment
Thickened Mucus
Recurrent Pulmonary Infections
Pulmonary Congestion
Pancreatic Insufficiency
Steatorrhea
Fat-Soluble Vitamin Deficiencies
Salty Taste to Skin
Meconium Ileus
Delayed Growth and Poor Weight Gain
2 mins
Cystic Fibrosis Interventions
Bronchodilators
N-Acetylcysteine (Mucolytics)
Inhaled Hypertonic Saline
Early Antibiotics
Dornase Alfa (Mucolytic Agent)
Postural Drainage with Percussion
Fat Soluble Vitamin Supplements
Pancreatic Enzymes with Every Meal
High Protein, High Calorie Diet
Added Dietary Salt
Glucose Monitoring
2 mins
Cystic Fibrosis Mechanisms
Autosomal Recessive
CFTR Chromosome 7
Cl- channel Defect
Decreased Chloride Secretion
Increased Na and Water Reabsorption
Increased Na and Cl in Sweat
Dehydration of Mucous Layers
2 mins
Cystic Fibrosis Symptoms and Complications
Recurrent Pulmonary Infections
Chronic Bronchitis
Nasal Polyps
Pancreatic Insufficiency
Intestinal Obstruction
Malabsorption and Diarrhea
Vitamin Deficiencies
Chronic Hepatic Disease
Infertility in Males
1 min
Kawasaki Disease
Pathophysiology
Prevalent in Asian Children
Necrotizing Vasculitis
Signs and Symptoms
Fever
Strawberry-Red Tongue and Mucosa
Lymphadenopathy
Desquamative Skin Rash
Erythema and Edema of the Hands and Feet
Conjunctivitis
Coronary Aneurysm
Treatment
Intravenous Immunoglobulin (IVIG)
Aspirin
2 mins
Kawasaki Disease
Prevalent In Asian Children
Necrotizing Vasculitis
fever
Erythema And Edema Of The Hands And Feet
Conjunctivitis
Aspirin
t cell mediated
Coronary Aneurysm
Myocardial Infarction
Wilms' Tumor (Nephroblastoma)
Cause
Malignant Renal Tumor
Assessment
Abdominal Mass
Hematuria
Fever
Hypertension
Interventions
Nephrectomy
Chemotherapy
Radiation
Considerations
Do Not Palpate Abdomen
Children Under 5 Years Old
2 mins
Abnormal curvatures of the Penis
Chordee Penis is a Ventrally folded, poorly developed Penis
Chordee Associated with hypospadias
Peyronie's disease
Peyronie's disease due to subq fibrosis of penis
Peyronie disease- fibrosis specifically of the Tunica Albuginea
hypospadias- must wait to circumcise for 6 mos
Imperforate Anus
Mechanism
Congenital Anorectal Malformation
Signs and Symptoms
No Anal Opening
Absence of Meconium
Gradual Increase in Abdominal Distention
Considerations
Surgical Repair
Bowel Management
2 mins
Cleft Lip or Palate Interventions
Considerations
Encourage Bonding
Prosthodontic Device
Modified Nipple
Burping
Surgical Repair
Normal Saline Rinse
Elbow Restraints
Avoid Rigid Eating Utensils
2 mins
Patent Ductus Arteriosus
Continuous
Machine like murmur
Often Due to Congenital Rubella
Prematurity
1 min
Tetralogy of Fallot (TOF)
Features
Blue Baby Syndrome
Mechanism
PROVe Acronym
Pulmonary Infundibular Stenosis
Right Ventricular Hypertrophy
Overriding Aorta
Ventricular Septal Defect (VSD)
Diagnosis and Treatment
Boot-Shaped Heart
Squatting for Tet Spells
Surgery
2 mins
Torsades de Pointes
Characteristics
Polymorphic Ventricular Tachycardia
Prolonged QT Interval
QRS Twist Around Isoelectric Line
Causes
Congenital
Antibiotics
Antiarrhythmics
Antipsychotics
Antidepressants
Electrolyte Deficiencies
Complications
Ventricular Fibrillation
Treatment
Stable: Magnesium Sulfate
Unstable: Defibrillation
3 mins
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