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Wayne Shared "Pathology Bliss 6/14/2024" - 33 Picmonics

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Pathology Bliss 6/14/2024

COPD Overview (Chronic Obstructive Pulmonary Disease Overview)
Causes
Inhaled Toxins
Smoking
AAT Deficiency
Assessment
Emphysema
Chronic Bronchitis
Asthma
Considerations
Spirometry
Slow Progression
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2 mins
Emphysema
Clinical Features
Pink Puffer
Exhale through Pursed Lips
Barrel Chest
Pathophysiology
Obstructive Lung Disease
Increased Lung Compliance
Types
Centriacinar
Panacinar
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2 mins
Alpha 1 Antitrypsin Deficiency
Characteristics
Decreased Alpha Anti Trypsin
Increased Elastase Activity
Decreased Elastic Tissue
Misfolded Protein Aggregates
PAS+ Globules
Clinical Features
Panacinar Emphysema
Dyspnea
Cirrhosis
Hepatocellular Carcinoma
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2 mins
Asthma
Obstructive lung disease
Bronchial Hyperresponsiveness
History of Atopic Disease
Beta2 agonists
Corticosteroids
Curschmann's spirals
Hypertrophy of smooth muscle
Reversible
Charcot Leyden crystals
Methacholine challenge
Wheezing
Cough
Initially decreased PaCO2
Pulsus paradoxus
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2 mins
Bronchiectasis
Obstructive Lung Disease
Chronic Necrotizing Infection
Permanent Airway Dilation
Poor Ciliary Motility
Kartagener's Syndrome
Cystic Fibrosis
Allergic Bronchopulmonary Aspergillosis
Hemoptysis
Increased Sputum
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2 mins
Obstructive Lung Disease
Blocked Airflow
Increased residual volume
V/Q Mismatch
Decreased forced vital capacity (FVC)
Decreased FEV1/FVC ratio
Asthma
Bronchiectasis
Chronic bronchitis
Emphysema
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51 secs
Kartagener Syndrome (Primary Ciliary Dyskinesia)
inheritance pattern
Autosomal Recessive
pathogenesis
Immotile Cilia Due to a Dynein Arm Defect
Symptoms
Decreased Male and Female Fertility
Immotile Sperm
Dysfunctional Fallopian Tube Cilia
Increased Risk of Ectopic Pregnancy
Bronchiectasis
Recurrent Sinusitis
Chronic Ear Infections
Conductive Hearing Loss
Situs Inversus (Dextrocardia on Chest X-Ray)
SCreening
Decreased Nasal Nitric Oxide Used as Screening Test
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5 mins
Idiopathic Pulmonary Fibrosis
Interstitial Restrictive Lung Disease
Age over 50 years, Males, Tobacco
CLINICAL FEATURES
Dyspnea and Cough
Fatigue
Crackles
Digital Clubbing
DIAGNOSIS
Bronchiectasis
Honeycomb Pattern
Restrictive Pattern
COMPLICATIONS
Respiratory Failure
Right Heart Failure
TREATMENT
Oxygen
Antifibrotic Medications
Lung Transplant
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5 mins
Pneumoconioses
Apex of Lung
Coal
Caplan Disease
Macrophages --> Antracosis
Silica (Sand)
Impairs Phagolysosome Function
Increased risk of Tuberculosis
Eggshell Calcification on Hilar Lymph Nodes
Berryliosis
Aerospace Workers
Non-Caseating Granulomas
Resembles Sarcoidosis
Base of Lung
Asbestos
Asbestos Bodies
Bronchogenic Carcinoma
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Coal Workers Pneumoconiosis
Risk Factor
Prolonged Coal Exposure
Characteristics
Black Lung Disease
Upper Lobes
Pathophysiology
Restrictive Lung Disease
Dust-Laden Macrophages
Inflammation and Fibrosis
Imaging
Small, Rounded Nodular Opacities
Consideration
Caplan Syndrome
Anthracosis
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2 mins
Asbestosis Characteristics and Presentation
Characteristics
Pneumoconiosis
Restrictive Lung Disease
Lower Lobes
Risk Factors
Shipbuilding
Roofing
Smoking
Plumbing
Clinical Features
Dyspnea with Exertion
Cough
Digital Clubbing
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3 mins
Pulmonary Hypertension Classification (WHO)
Group 1
Pulmonary Arterial Hypertension
Idiopathic
Hereditary
BMPR2 Mutation
Group 2
Left Heart Disease
Group 3
Lung Diseases or Hypoxia
COPD
Obstructive Sleep Apnea
Group 4
Chronic Pulmonary Emboli
Group 5
Multifactorial
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2 mins
Adenocarcinoma of the Lung
Characteristics
Most Common Lung Cancer
Most Common in Nonsmokers
Peripheral Location
KRAS, EGFR, and ALK Mutations
Diagnosis
Glandular Pattern
Often Stains with Mucin
Clinical Features
Presents with Hemoptysis
Clubbing
Treatment
Surgical Resection
Chemotherapy and Radiation
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2 mins
Pancoast Tumor
Characteristics
Apical Lung Tumor
Non-small Cell Lung Cancer
Clinical Features
Axillary or Shoulder Pain
Hoarseness
Horner Syndrome
Superior Vena Cava Syndrome
Sensorimotor Deficits
Hemidiaphragm Paralysis
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1 min
Bronchial Carcinoid Tumor
Characteristics
Excellent Prognosis
Signs and Symptoms
Symptoms of Bronchial Obstruction
Often Asymptomatic
Carcinoid Syndrome
Diarrhea
Wheezing
Flushing
Diagnosis
5-HIAA in Urine
Nests of Neuroendocrine Cells
Chromogranin A Positive
Treatment
Surgical Resection
Octreotide for Symptomatic Relief
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2 mins
Tension Pneumothorax
Mechanism
Air Enters Pleural Space, but Can't Exit
Trauma or Infection
Signs and Symptoms
Decreased Breath Sounds
Trachea Deviates Away from Affected Side
Chest Pain
Tachycardia
Tachypnea
Hypotension
Hypoxemia
Hyperresonance
Emergency
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2 mins
Pneumothorax
Mechanism
Air Enters Pleural Space
Assessment
Sudden Dyspnea
Absent or Restricted Movement on Affected Side
Decreased or Absent Breath Sounds on Affected Side
Chest Pain
Tracheal Deviation
Vital Sign Changes
Crepitus
Considerations
High Fowler's Position With Oxygen
Prepare For Chest Tube Placement
Educate High Risk Patients
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2 mins
Potter Sequence
PATHOGENESIS
Oligohydramnios
clinical findings
Limb Deformities
Facial Anomalies
Pulmonary Hypoplasia (Most Common Cause of Death)
Etiologies
Autosomal Recessive Polycystic Kidney Disease (ARPKD)
Posterior Urethral Valves
Chronic Placental Insufficiency
Bilateral Renal Agenesis
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3 mins
Oligohydramnios
Decreased Amniotic Fluid
Etiologies
Renal Agenesis (Fetal Urinary Tract Abnormalities)
Uteroplacental Insufficiency
Premature Rupture of Membranes (PROM)
Diagnosis
Ultrasound
Amniotic Fluid Index (AFI) < 5 cm
Complications
Spontaneous Abortion
Pulmonary Hypoplasia
Musculoskeletal Abnormalities
Intrauterine Growth Restriction (IUGR)
Treatment
Treat Underlying Cause
Delivery (When Viable)
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2 mins
Autosomal Dominant Polycystic Kidney Disease
Characteristics
Autosomal Dominant
Mutations in PKD1/2
Cystic Enlargement of Renal Tubules
Clinical Features
Chronic Kidney Disease
Hypertension
Mitral Valve Prolapse
Hepatic Cysts
Berry (Saccular) Aneurysms
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3 mins

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Wayne Shared Pathology Bliss 6/14/2024 - 33 Picmonics